[N-clex] cystic fibrosis

: exocrine gland(외분비선) 분비↓(막히거나 분비가 원활하지 않음)

- 상염색체 열성

- malabsortion(tinning hair) : 면역↓, 감염↑

- sweat chloride test(non invasive) : 40↓:normal / 40~60:suggestive / 60↑:confirm

- foul smell stool

- steatorrhea(지방변)

- COPD같은 증상(dyspnea, barrled chest)

- 지용성 Vit 흡수↓ (water misible(섞이는) 가능)

Tx)

- flutter valve : secretion 배출(공 호루라기?)

- enzyme : with meal or before meal 30min / after X

- 확인법 : short(대변 2~3회/d), long(Wt gain)

- high calorie, protein